Q Autopsy finding in a patient who dies of Tetrology of Fallot is
a) Brachiocephalic vein draining into the left renal vein b) Inferior vena cava (IVC) draining to the superior mesenteric vein c) Atrial Septal Defect (ASD) d) Decreased vascularity of the lung field
d) Left ventricular end diastolic pressure of 20 mm Hg
24) d
Fontan procedure is for tricuspid atresia and is done when there is low pulmonary vascular resistance. For the same reason it is not done in neonates.
In Tricuspid atresia, venous blood does not go to right ventricle and there is mixing of venous and arterial blood in aorta which leads to decreased oxygenation.
Most infants with tricuspid atresia have restrictive pulmonary blood flow. To improve systemic oxygentaion they undergo modified Blalock-Taussig shunt, which is a small polytetrafluoroethylene (PTFE) graft to connect the subclavian artery and a pulmonary artery.
Criteria for Fontan procedure are
Age older than 4 years
Sinus rhythm
Normal systemic venous return
Normal right atrial volume
Mean pulmonary artery pressure less than 15 mm
Pulmonary arteriolar resistance less than 4 Wood units/m 2
Pulmonary artery–aorta ratio more than 0.75
Left ventricular ejection fraction more than 0.60
Current absolute contraindications are a pulmonary vascular resistance above 4 Wood units/m2, severe hypoplasia of the pulmonary arteries, and severe diastolic dysfunction of the left ventricle.
Q) Least useful investigation in a patient with recurrent Lower GI bleed, multiple upper and lower GI endoscopies negative?
a) BMFT
b) Double balloon enteroscopy
c) Capsule endoscopy
d) Push endoscopy
Answer: a) BMFT
Investigations in lower GI bleed should be specific and less time consuming.
Small bowel enteroclysis (BMFT), which uses barium and contrast infusion, has a very low yield and is poorly tolerated, hence rarely used.
Capsule endoscopy is excellent for stable patients, with success rates up to 90% in detecting small bowel pathology. Push enteroscopy can reach 50–70 cm beyond the ligament of Treitz and permits both diagnosis and therapy; success ~40%. Double-balloon enteroscopy provides complete small bowel evaluation and allows biopsy and therapy, with yield 77–85%.
Therefore, BMFT is the least useful investigation.
Q) Elderly healthy male with impacted denture. Removed endoscopically. Pt developed fever, dyspnoea and respiratory distress over 24 hrs. X-ray revealed Lt hydrothorax and mediastinal emphysema.
a) ICD and NG feeds
b) ICD and TPN
c) Cervical esophagectomy, FJ, debridement, ICD
d) Debridement, primary repair with buttress and ICD